Abstract

Parachordoma, also named as myoepithelioma, is a rare,non axially located soft tissue tumor histologically resembling chordoma. This rare entity is also named as extra axial chordoma, parachordoma and chordoma periphericum. Lesions are generally seen in male patients and located at the lower extremities. The primary treatment modality is surgery. Even this tumor is benign, it may show local aggressive potential. Late local recurrences can be expected and pulmoner metastases are seldom. In this case presentation, a rare parachordoma case located at the distal femur is evaluated.