Hemoptysis as a presentational finding of intrathoracic paravertebral mass of extramedullary erythropoiesis in a patient with β-thalassemia intermedia

Intrathoracic extramedullary erythropoiesis (EME) is a rare but well-known complication of β-thalassemia intermedia. Patients with intrathoracic EME are generally asymptomatic. Herein, we report an adult patient with β-thalassemia intermedia who was diagnosed to have intrathoracic EME masses and presented with hemoptysis. Upto our knowledge, hemoptysis has not been reported previously as a presentational complaint among patients with β-thalassemia who have thoracal EME masses. Initiation of chronic transfusion programme and hydroxurea treatment caused regression in the masses, in addition to disappearance of the complaint of hemoptysis. Hemoptysis should be kept in mind as a rare finding of of EME in β-thalassemia intermedia.

Beta talasemi intermedia tanýlý bir hastada ekstramedüller eritropoeze ikincil intratorasik paravertabral kitlelerin baþvuru bulgusu olarak hemoptizi

Ýntratorasik ekstramedüller eritropoez beta talasemi intermedianýn nadir ama iyi bilinen bir komplikasyonudur. Ýntratorasik ekstramedüller eritropoezi olan hastalar genellikle asemptomatiktir. Burada beta talasemi intermedia tanýsýyla izlenirken hemoptizi ile baþvuran ve sonrasýnda intratorasik ekstramedüller eritropoez kitleleri tespit edilen bir eriþkin vaka sunulmaktadýr. Torakal ekstramedüller eritropoez kitleleri olan beta talasemi hastalarýnda hemoptizi ile baþvuru daha öncesinde bildirilmemiþtir. Hastanýn eritrosit transfüzyon programýna alýnmasý ve hidroksiüre tedavisinin baþlanmasý ile hem hemoptizi þikayeti kaybolmuþ hem de kitleleri küçülmüþtür. Beta talasemi intermedia tanýlý hastalarda hemoptizi intratorasik ekstramedüller eritropoezin bir bulgusu olarak akýlda bulundurulmalýdýr.